Case report

A 22-year-old woman (G1P0), with a noncontributive family history and negative history of administration of teratogenic drugs, was referred to our antenatal unit at 23 weeks for an ultrasonographic examination. During our examination we could observe following findings:

• Hypoplastic right ventricle of the heart with a hypertrophy of its wall and tricuspid valve atresia;

• Membranous interventricular septal defect;

• Hypoplasia of the pulmonary artery.

The parents opted for the continuation of the pregnancy and an amniocentesis was done, revealing a normal karyotype. The findings were confirmed after delivery.

Images 1, 2: The images show a hypoplastic right ventricle of the heart seen at the level of the four-chamber view. Tricuspid valve was atretic.

Images 3, 4: Gray scale (Images 3) and power Doppler (Image 4) images comparing the size of the hypoplastic right ventricle and normal left ventricle of the heart at the level of the four-chamber view. A small membranous interventricular septal defect of the heart is visible at the image 4.

Images 5, 6: Gray scale (Images 5) and power color (Image 6) images comparing the size of the hypoplastic pulmonary artery and normal sized aorta.

Image 7: Gray scale image comparing the size of the hypertrophic right ventricular wall (calipers 2) and normal thickness of the left ventricular wall (calipers 1) of the heart measured at the level of the four-chamber view.

Video 1: The video shows the hypoplastic right ventricle with the tricuspid atresia seen at the level of the four-chamber view.