situs ambiguous with dextrocardia, transposition of great arteries, cardiac total anomalous pulmonary venous connection
Fabien Ho
on 07/22/2024
on Monday, July 22nd, 2024
Dear community of the fetus.net,
About the cardiac malformation :
Since the pulmonary veins drains into the atrium (with left morphology) then into a ventricle (right morphology) then into the aorta : is is like LA -> RV -> Aorta :
Same : SVC and IVC -> LV -> Pulm arteries
Could you call that a corrected Transposition of great arteries ?
French people used to call that double discordance, because atrioventricular discordance + ventriculo arterial discordance.
About the heterotaxy :
to know if it is left of right heterotaxy, need to check the spleen, and IVC.
Basically : polysplenia + IVC interrupted contuing with azygos vein = left isomerism.
Asplenia = right isomerism
About the cardiac malformation :
Since the pulmonary veins drains into the atrium (with left morphology) then into a ventricle (right morphology) then into the aorta : is is like LA -> RV -> Aorta :
Same : SVC and IVC -> LV -> Pulm arteries
Could you call that a corrected Transposition of great arteries ?
French people used to call that double discordance, because atrioventricular discordance + ventriculo arterial discordance.
About the heterotaxy :
to know if it is left of right heterotaxy, need to check the spleen, and IVC.
Basically : polysplenia + IVC interrupted contuing with azygos vein = left isomerism.
Asplenia = right isomerism