Cardiac anomalies, including right ventricular outflow tract obstruction (RVOTO) or twin circular intracardiac shunt typically affect recipient twin. Interestingly, in our case the donor was affected.
Laser intervention at an early stage of TTTS associated with a significant reduction in the incidence of RVOTO. A prediction model for the risk of RVOTO at birth in TTTS recipients was constructed - abnormal flow in the DV, pericardial effusion and early gestational age at onset of TTTS are predictors of RVOTO in TTTS recipients (Eschbach SJ et al., 2017), .
RVOTO can develop after laser treatment or even in the neonatal period and in all Quintero stages (Eschbach SJ et al., 2018), .
Donor twin is rarely affected by the RVOTO and the pathomechanism of this phenomenon in donor twin is still not fully clarified.
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