Immef – Instituto da Mulher e Medicina Fetal de Curitiba – Curitiba – PR – Brasil

Case report:

A 27-year-old women (G2Ab1) was referred to our fetal medical unit for routine prenatal ultrasound at 23+5 weeks. There was no known family history of congenital disease.

We diagnosed an isolated right aortic arch with left ductus arteriosus. The aorta was on the right of the trachea and pulmonary trunk and ductus arteriosus were on the left. These vessels formed a vascular ring around the trachea (“U-sign").

No other associated findings were detected on the ultrasound examination. 

Image 1, 2: Normal left ventricular outflow tract view but right-deviated aorta and 4-chamber view

Image 3, 4: Four-chamber view; Doppler Ultrasound showed normal flow through atrio-ventricular valve.

Image 5-8: The aorta was on the right of the trachea (Tr), pulmonary trunk (PA) and ductus arteriosus(DA) were on the left. These vessels formed a vascular ring around the trachea.

Image 9, 10: The outflow of aortic artery from left ventricular and right aortic arch.

Image 11, 12: Aortic arch; and 3 -vessel view: superior vena cava (VCS) ; Aorta (Ao) , Pulmonary artery (PA) ; Trachea (Tr)

Video 1-3: The aorta was on the right of the trachea and pulmonary trunk and ductus arteriosus were on the left. These vessels formed a vascular ring around the trachea.